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A rare case of cellular angiofibroma of the vulva in a 51-ys-old woman is presented. It was a 1.5 cm tumour of the right maior labium. Histological and immunohistochemical findings were similar to those described previously. The tumour cells expressed vimentin, CD99, estrogen and progesterone receptor. They were negative for EMA, desmin, h-caldesmon, S100 protein, CD34, CD10, and bcl-2. Besides the case presentation, differential diagnosis and histogenesis of angiomyxoid lesions of the lower genital tract is discussed, and a brief overview of the literature is added.
Keywords: angiomyofibroblastoma, cellular angiofibroma, spindle cell lipoma, superficial myfibroblastoma, vulva